A Case of Septic Arthritis in Patient with Wiskott-Aldrich Syndrome

Ju-Ho Do

doi:10.4078/jkra.2007.14.2.149

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Do: A Case of Septic Arthritis in Patient with Wiskott-Aldrich Syndrome

Original Article

J Korean Rheum Assoc 2007;14(2):149-153.

Published online: 23 June 2007

DOI: https://doi.org/10.4078/jkra.2007.14.2.149

A Case of Septic Arthritis in Patient with Wiskott-Aldrich Syndrome

Ju-Ho Do, M.D.

Department of Rheumatology, Dong-San Hospitlal, Keimyung University School of Medicine, Daegu, Korea

Received 11 January 200716 February 2007

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Abstract

The Wiskott-Aldrich syndrome is a rare disease characterized by thrombocytopenia, recurrent eczema and a marked vulnerability to recurrent infection. Patients with Wiskott-Aldrich syndrome have frequent infections by bacteria which have polysaccharide capsules such as Pneumo- coccus, Hemophilus influenzae and Neisseria meningitidis due to poor antibody response to polysaccharide antigens. We experienced a 21 years old man with septic arthritis combined with Pneumococcal pneumonia, multifocal abscesses in back and iliacus muscle. After treatment with antibiotics for one month, he was treated successfully.

Keywords: Wiskott-Aldrich syndrome, Infection, Septic arthritis

REFERENCES

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Fig. 1.

(A) Chest radiograph shows increased infiltration of right lower lobe. (B) Infiltration was disappeared after antibiotic treatment.

Fig. 2.

(A) CT scan of right shoulder joint shows joint effusion with synovial enhancement (arrow). (B) Joint effusion was disappeared after antibiotic treatment.

Fig. 3.

(A) CT scan of pelvis shows multifocal abscesses of right back muscle and iliacus muscle (arrows). (B) Abscesses were disappeared after antibiotic treatment.

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