Journal List > J Korean Rheum Assoc > v.14(2) > 1003552

Do: A Case of Septic Arthritis in Patient with Wiskott-Aldrich Syndrome

Abstract

The Wiskott-Aldrich syndrome is a rare disease characterized by thrombocytopenia, recurrent eczema and a marked vulnerability to recurrent infection. Patients with Wiskott-Aldrich syndrome have frequent infections by bacteria which have polysaccharide capsules such as Pneumo- coccus, Hemophilus influenzae and Neisseria meningitidis due to poor antibody response to polysaccharide antigens. We experienced a 21 years old man with septic arthritis combined with Pneumococcal pneumonia, multifocal abscesses in back and iliacus muscle. After treatment with antibiotics for one month, he was treated successfully.

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Fig. 1.
(A) Chest radiograph shows increased infiltration of right lower lobe. (B) Infiltration was disappeared after antibiotic treatment.
jkra-14-149f1.tif
Fig. 2.
(A) CT scan of right shoulder joint shows joint effusion with synovial enhancement (arrow). (B) Joint effusion was disappeared after antibiotic treatment.
jkra-14-149f2.tif
Fig. 3.
(A) CT scan of pelvis shows multifocal abscesses of right back muscle and iliacus muscle (arrows). (B) Abscesses were disappeared after antibiotic treatment.
jkra-14-149f3.tif
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