Journal List > Tuberc Respir Dis > v.62(3) > 1001070

Lim, Hong, Shin, Kim, Jee, Myoung, Park, and Park: A Case of Primary Pulmonary Artery Sarcoma Mimicking Pulmonary Embolism: Role of PET/CT for Differential Diagnosis

Abstract

Primary pulmonary artery sarcoma is a rare malignant tumor arising from the pulmonary artery. Diagnosis of primary pulmonary artery sarcoma is quite difficult and the conditon is often misdiagnosed as a more common disease, such as a pulmonary embolism. PET can help in diagnosing a pulmonary artery sarcoma due to the increased uptake of 18F-FDG in the area of the tumor. However, the poor anatomic resolution of PET has limited its clinical applications in pulmonary vascular disease. The recently developed PET/CT is the fusion of PET and CT that improves the anatomical resolution of PET. We report a case of a primary pulmonary artery sarcoma mimicking a pulmonary embolism that was diagnosed with PET/CT and confirmed with a surgical resection.

Figures and Tables

Figure 1
Chest PA shows ill defined consolidation and ipsilateral pleural effusion in right hemithorax.
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Figure 2
CT scan shows a soft tissue mass in right main pulmonary artery and ipsilateral pleural effusion.
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Figure 3
PET(A), CT(B), and fusion of PET and CT (PET/CT)(C) shows FDG uptake at right main pulmonary artery(arrow).
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Figure 4
Exisioned lung shows yellowish round mass obstructing right main pulmonary artery(A) and histologic finding shows malignant fibrous histiocytoma with a background of spindle cells in a storiform configuration and giant cells (H&E staining, ×400)(B).
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