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Joo, Oak, Lee, Jang, Kim, Lee, Song, Park, Moon, Lee, and Kim: A Case of Tracheobronchomegaly with Pneumonia
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Tuberculosis and Respiratory Diseases

Tuberculosis and Respiratory Diseases 2006; 61(4): 403-406.

Published online: 31 October 2006

DOI: https://doi.org/10.4046/trd.2006.61.4.403

A Case of Tracheobronchomegaly with Pneumonia

Kyu Re Joo, M.D., Ju Hyun Oak, M.D., Sung Eun Lee, M.D., Suk Tae Jang, M.D., Sung Kyoung Kim, M.D., Sang Haak Lee, M.D., Jeong Sup Song, M.D., Sung Hak Park, M.D., Hwa Sik Moon, M.D., Bae Young Lee, M.D.1, Hyeon Sook Kim, M.D.1

Department of Internal Medicine, The Catholic University of Korea, College of Medicine, Seoul, Korea.

1Department of Radiology, The Catholic University of Korea, College of Medicine, Seoul, Korea.

Address for correspondence : Hwa Sik Moon, M.D. Department of Internal Medicine, St. Paul's Hospital, The Catholic University of Korea, 620-56, Jeonnong-dong, Dongdeamoon-gu Seoul, 130-709, Korea. Phone: 82-2-958-2463 Fax: 82-2-968-7250, hsmoon@catholic.ac.kr

Received 16 June 2006       Accepted 18 July 2006

Copyright © 2006 The Korean Academy of Tuberculosis and Respiratory Diseases

Abstract

A 66-years-old man was refered to our hospital because of cough, sputum, chill and fever. Enlargement of the trachea and main bronchi on radiography and bronchoscopy is compatible with Mounier-Kuhn syndrome. Mounier-Kuhn syndrome or tracheobronchomegaly is a rare disorder of uncertain etiology, characterized by marked dilatation of the trachea and major bronchi. This syndrome is associated with tracheal diverticulosis, bronchiectasis and recurrent respiratory tract infection.
We report a rare case of Mounier-Kuhn syndrome with pneumonia and literature reviews.

Keywords: Mounier-Kuhn syndrome, Tracheobronchomegaly

Figures and Tables

Figure 1
Chest X-ray shows ill-defined infiltrations in the right lower lobe. Dilatation of trachea and both bronchi are noted.
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Figure 2
Chest CT scan in axial plane at the level of aortic arch shows dilatation of trachea, septation(arrowhead) in trachea and adjacent diverticula(arrow)(A). Ill-defined consolidation and small nodules are noted in right lower lobe(B).
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Figure 3
Chest CT scan in coronal plane shows tracheomegaly and bronchomegaly(A). In three dimensional reconstruction CT bronchogram, anterior view(B) and lateral view(C) show diverticula(arrowhead).
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Figure 4
Bronchoscopy shows the a divercitulum in posterior wall of trachea at the level of 5cm below vocal cord. There was some secretions in this diverticulum(A). This secretions were disappeared after bronchoscopic suction(B). This images were reconstructed by CT virtual bronchoscopy(C). Arrow points this diverticulum(C).
trd-61-403-g004

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