Pagets disease has been well known disease in western countries, but it is extremely rare in orient and no case has been reported in Korea yet. It is a chronic osseous disease affecting middle and late life, characterized by progressive skeletal deformities which consist of excessive resorption and abnormal regeneration. We experienced a case of Paget's disease in a 57-year old man with involvement of pelvis, femur and skull, and confirmed with open biopsy.