Journal List > Korean J Pediatr Gastroenterol Nutr > v.5(1) > 1110450

Korean J Pediatr Gastroenterol Nutr. 2002 Mar;5(1):113-117. Korean.
Published online Mar 31, 2002.  https://doi.org/10.5223/kjpgn.2002.5.1.113
Copyright © 2002 The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition
A Case of Cholangiocarcinoma Arising from Type I Choledochal Cyst in a 13-year-old Girl
Sung Ryon Ahn, Sang Ook Nam, Jae Hong Park, Young Tak Lim, Jun Woo Lee,1 and Chang Hun Lee2
Department of Pediatrics, College of Medicine, Pusan National University, Busan, Korea.
1Department of Radiology, College of Medicine, Pusan National University, Busan, Korea.
2Department of Pathology, College of Medicine, Pusan National University, Busan, Korea.
Abstract

Choledochal cyst is a rare developmental malformation of the biliary tree and has serious problem of transformation to malignancy. The development of cholangiocarcinoma related to choledochal cyst increases as the age of patient increases and is more common in Orientals with female predominance of 2.5 times. Prevalence rate of cholangiocarcinoma is various from 2.5 to 15.6% in adult with choledochal cyst, but very low in children. We experienced a case of cholangiocarcinoma with multiple liver metastases arising from type I choledochal cyst in a 13-year-old girl who complained of sudden onset of right upper quadrant abdominal pain.

Keywords: Cholangiocarcinoma; Choledochal cyst; Child