Journal List > Endocrinol Metab > v.27(2) > 1085947

Park, Oh, Shon, Kim, Jeon, and Jung: A Case of Dopamine-Secreting Pheochromocytoma


A pheochromocytoma is a neuroectodermal tumor that originates from the chromaffin cells of the sympathetic system. It has typical symptoms or signs, such as periodic attacks of paroxysmal hypertension, palpitation, headache, and sweating, related to an increased catecholamine secretion. Types of catecholamine secreted from tumors are usually norepinephrine and epinerphrine. There are a few reports of dopamine-secreting pheochromocytoma with absence of other catecholamines secretion. Here, we report the case of a 59-year-old man with dopamine-secreting pheochromocytoma, with no typical symptoms or signs.

Figures and Tables

Fig. 1
Dynamic adrenal gland computed tomography. 2.7 cm-sized right adrenal mass is seen on pre-enhance phase (A) and arterial phase (B). Adrenal adenoma is highly suspicious.
Fig. 2
I131-MIBG scan. No evidence of significant radiotracer uptake in computed tomography-detected right adrenal mass. Lt, left; Rt, right.
Fig. 3
Histology. Dopamine-secreting pheochromocytoma (A) shows more strong staining than typical pheochromocytoma (B) and normal adrenal medulla (C) (dopamine IHC stain, × 200).


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