The Sertoli-Leydig cell tumor is a rare sex cord-stromal tumor of the ovary, accounting for less than 0.5% of all primary ovarian neoplasm. They occur predominantly in the second and third decades, rarely before puberty or after the menopause. The most common symptom is menstrual disorder including vaginal bleeding and occasionally masculinization is accompanied with this symptom. This symptom is the results of excessive testosterone production of Leydig cell, but approximately 50% of patients with Sertoli-Leydig cell tumor have no endocrine manifestations. The majority of these tumors are benign and almost all are localized unilaterally. Prognosis proves generally favorable with 5-year survival rate of 70~90%. Recurrence is rare. We have experienced a case of intermediately differentiated Sertoli-Leydig cell tumor accompanied with multiple uterine leiomyomas in a 30 years old woman who had oligomenorrhea, hirsutism and infertility. We report this case with a brief review of literature.