kjcn Korean Journal of Community Nutrition Korean J Community Nutr 1226-0983 2287-1624 Journal of the Korean Society of Community Nutrition 10.14253/KJCN.2015.17.1.38 kjcn-17-38 Original Article The Abnormalities in Neuro-Imaging and Somatosensory Evoked Potentials in Hirayama Disease ParkJin-Sung 1 LeeSang-Hoon 2 Department of Neurology, Kyungpook National University School of Medicine, Daegu, Korea Department of Radiology, Kyungpook National University Medical Center, Daegu, Korea Address for correspondence; Jin-Sung Park Department of Neurology, Kyungpook National University Hospital, 680 Gukchaebosang-ro, Jung-gu, Daegu 700-842, Korea Tel: +82-53-200-2753 Fax: +82-53-200-2168 E-mail: jinforeva@gmail.com 122015 18122015 171 3840 12112014 06022015 26022015 Copyright © 2015 Journal of the Korean Society of Community Nutrition 2015 This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/3.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited. Hirayama disease Magnetic resonance imaging Evoked potentials REFERENCES Tashiro K Kikuchi S Itoyama Y Tokumaru Y Sobue G Akiguchi I Nationwide survey of juvenile muscular atrophy of distal upper extremity (Hirayama disease) in Japan Amyotroph Lateral Scler 20067 3845 Zhou B Chen L Fan D Zhou D Clinical features of Hirayama disease in mainland China Amyotroph Lateral Scler 201011 133139 Sonwalkar HA Shah RS Khan FK Gupta AK Bodhey NK Vottath S Imaging features in Hirayama disease Neurol India 200856 2226 Hassan KM Sahni H Jha A Clinical and radiological profile of hirayama disease: a flexion myelopathy due to tight cervical dural canal amenable to collar therapy Ann Indian Acad Neurol 201215 106112 Yin B Liu L Geng DY Features of Hirayama disease on fully flexed position cervical MRI J Int Med Res 201139 222228 Finsterer J Loscher W Wanschitz J Baumann M Quasthoff S Grisold W Hirayama disease in Austria Joint Bone Spine 201380 503507 Wang XN Cui LY Liu MS Guan YZ Li BH DU H A Clinical neurophysiology study of Hirayama disease Chin Med J (Engl) 2012125 11151120 Figures

Cervical magnetic resonance imaging (MRI) and right median somatosensory evoked potentials (SEP) of the patient. The T2 weighted MRI with neck in neutral position was unremarkable while T2 weighted MRI with neck in flexion shows anterior displacement of the posterior dural sac (A, B). The reversible inter-peak latency between N13 and N19 on supine (5.5 ms) (C) and flexed (7.45 ms) (D) somatosensory evoked potentials (SEP) in the symptomatic side also support the diagnosis of Hirayama disease. (Normal SEP interpeak latency < 6.59 ms).