Journal List > J Korean Orthop Assoc > v.48(4) > 1013245

Yoon and Chung: Sprengel Deformity with Bilateral Huge Omovertebra

Abstract

Sprengel's deformity is characterized by the congenital migration of the scapula superiorly in relation to the thoracic cage. Other congenital anomalies, such as Klippel-Feil syndrome, may occur in combination with Sprengel's deformity. We report on a case of Sprengel's deformity with a huge bilateral omovertebrae, which was combined with the clinical features of Klippel-Feil syndrome, including cervical fusion, short neck, low posterior hairline, and limitation of neck motion. However, no other deformities or functional defects were observed.

Figures and Tables

Figure 1
Sprengel's deformity can be seen on both sides. Abduction of the left shoulder is limited.
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Figure 2
Computed tomography of the upper chest showed cervical fusion and bilateral Sprengel's deformity with omovertebra.
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Figure 3
The size of the pathologic specimens were: (A) 10×6 cm; (B) 9×4 cm.
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Figure 4
Postoperative result 15 months later showed stationary level of both scapulae.
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Figure 5
Postoperative result 15 months later showed an improved abduction of the left shoulder.
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