A Narrow Internal Auditory Canal with Duplication in a Patient with Congenital Sensorineural Hearing Loss
Hye Won Baik, MD,1Hyeon Yu, MD,1Kyung Soo Kim, MD,2
and Gi Hyeon Kim, MD1
1Department of Radiology, Chung-Ang University Hospital, College of Medicine, Chung-Ang University, Seoul 156-755, Korea.
2Department of Otolaryngology and Head and Neck Surgery, Chung-Ang University Hospital, College of Medicine, Chung-Ang University, Seoul 156-755, Korea.
Address reprint requests to: Hyeon Yu, MD, Department of Radiology, Chung-Ang University Hospital, College of Medicine, Chung-Ang University, 224-1, Heukseok-dong, Dongjak-gu, Seoul 156-755, Korea. Tel. (822) 6299-2647, Fax. (822) 6263-1557, Email: hyeonyu@cau.ac.kr
Received February 15, 2007; Accepted June 27, 2007.
Abstract
A narrow internal auditory canal (IAC) with duplication is a rare anomaly of the temporal bone. It is associated with congenital sensorineural hearing loss. Aplasia or hypoplasia of the vestibulocochlear nerve may cause the hearing loss. We present an unusual case of an isolated narrow IAC with duplication that was detected by a CT scan. In this case, the IAC was divided by a bony septum into an empty stenotic inferoposterior portion and a large anterosuperior portion containing the facial nerve that was clearly delineated on MRI.
Keywords: Ear, abnormalities, Ear anatomy, Ear, MR, Magnetic resonance (MR), pulse sequences, Magnetic resonance (MR), thin section, Nerves, abnormalities.
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